Desmoid tumors are a rare entity, histologically benign (fibroblastic proliferation) but with an infiltrative growth that gives them a local aggressive behavior1. The sporadic have an annual incidence of 2.4-4.6 per million inhabitants1, but their incidence increases in patients affected by familial adenomatous polyposis or Gardner’s syndrome. They are more frequent in women, and can be extra or intra-abdominal, the latter being the most frequent.
They affect the abdominal wall by 50%, retroperitoneum by 9% and the mesentery by 40%2. The description of tumors that depend on the intestinal wall is exceptional in the literature based on an exhaustive search in Pubmed and Cochrane with the key word “desmoid tumor small bowell” evidencing sporadic cases2.
Desenvolvido por Surya MKT